Persistent eustachian valve

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A rare congenital anomaly of the inferior vena cava characterized by the postnatal presence of an eustachian valve remnant which may be asymptomatic and considered a normal variant or prominent and clinically significant. Clinical presentation is variable and includes obstruction of the inferior vena cava cyanosis thrombosis pulmonary embolism infective endocarditis and when combined with persistent foramen ovale it may generate permanent right-to-left shunt.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version June 2024

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Persistent eustachian valve?

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Clinical Trials

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