Persistent left superior vena cava connecting to the roof of left-sided atrium

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Synonyms: Persistent left SVC connecting to left-sided atrium | Persistent left SVC connecting to the roof of left-sided atrium | Persistent left superior vena cava connecting to left-sided atrium

A rare congenital anomaly of superior vena cava characterized by a persistent left superior vena cava that drains into the left atrium through a direct connection to its roof creating a right-to-left shunt. Patients are at risk of developing chronic hypoxia decreased exercise tolerance cyanosis embolic cerebrovascular events and heart failure.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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Persistent left superior vena cava connecting to the roof of left-sided atrium?

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