A rare low-grade astrocytoma characterized by superficial location in the cerebral hemispheres with involvement of the meninges composed of GFAP-expressing cells showing nuclear and cytoplasmic pleomorphism and xanthomatous change surrounded by a reticulin network. The tumor corresponds to WHO grade II and typically affects children and young adults who often present with a long history of seizures. Extent of resection and mitotic index are important prognostic factors.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
Newly diagnosed with
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Pediatric Brain Tumor Foundation
The Pediatric Brain Tumor Foundation (PBTF) leads the way in ending the childhood cancer community’s biggest crisis through research funding, family support and advocacy. Dedicated wholly to addressing this rare, but devastating disease, we are guided by the experiences of patients, survivors, their parents, and siblings.
Moonshots for Unicorns
Curing single-gene disorders
COMBINEDBrain is a consortium for outcome measures and biomarkers for neurodevelopmental disorders. We are collaborating to cure rare, non-verbal brain disorders.
My Faulty Gene
My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.
My Little Sunshine Foundation
My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.
Educate and provide resources to POC with Rare Cancers
Help Hope Live
Help Hope Live assists individuals living with catastrophic injuries and illnesses to fundraise toward their medical expenses and related costs.
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