Pleuro-pericardial cyst

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Pleuro-pericardial cyst is a rare mostly congenital pericardium anomaly characterized by the presence of usually asymptomatic cysts which are typically located in the right costophrenic angle and are usually incidentally diagnosed. On occasion it manifests with chest pain dyspnea tachycardia persistent cough or cardiac arrhythmias. The condition is usually benign but rare complications such as cardiac tamponade cardiogenic shock mitral valve prolapse hoarseness atrial fibrillation right ventricular outflow tract obstruction spontaneous internal hemorrhage pulmonary stenosis and sudden death may occur.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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