Posttransplant acute limbic encephalitis

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Synonyms: PALE

Posttransplant acute limbic encephalitis is a rare acquired non-paraneoplastic limbic encephalitis disorder that develops in the setting of treatment-related immunosuppression typically after allogeneic hemapoietic stem cell transplantation characterized by onset of confusion headache anterograde amnesia seizures and/or loss of consciousness 2-6 weeks following transplantation. Bilateral non-enhancing T2 hyperintensities in limbic structures are observed on magnetic resonance imaging. Mild cerebrospinal fluid pleocytosis and syndrome of inappropriate antidiuretic hormone secretion may also be associated.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version May 2024

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