Posttransplant acute limbic encephalitis
Posttransplant acute limbic encephalitis is a rare acquired non-paraneoplastic limbic encephalitis disorder that develops in the setting of treatment-related immunosuppression typically after allogeneic hemapoietic stem cell transplantation characterized by onset of confusion headache anterograde amnesia seizures and/or loss of consciousness 2-6 weeks following transplantation. Bilateral non-enhancing T2 hyperintensities in limbic structures are observed on magnetic resonance imaging. Mild cerebrospinal fluid pleocytosis and syndrome of inappropriate antidiuretic hormone secretion may also be associated.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
Posttransplant acute limbic encephalitis?
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Help Hope Live
Help Hope Live assists individuals living with catastrophic injuries and illnesses to fundraise toward their medical expenses and related costs.
We are an international charity and the only resource of our kind in the world, dedicated to supporting those affected by encephalitis, their families and professionals involved in their care. Our work involves support, information, awareness and research.
Aicardi-Goutieres Syndrome Advocacy Association
AGSAA is a global coalition of deeply dedicated parent advocates working alongside clinicians, researchers, and scientists. We are united in our desire to improve the lives of individuals and families living with Aicardi-Goutières Syndrome and those yet to be diagnosed. Everything we do reflects a sense of urgency to rescue patient potential and preserve quality of life through accelerating research and providing timely emotional and educational support alongside evolving clinical care recommendations to affected families.
Moonshots for Unicorns
Curing single-gene disorders
COMBINEDBrain is a consortium for outcome measures and biomarkers for neurodevelopmental disorders. We are collaborating to cure rare, non-verbal brain disorders.
For a list of clinical trials in this disease area, please click here.