Primary angiitis of the central nervous system

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Primary angiitis of the central nervous system

Synonyms: Isolated angiitis of the central nervous system | PACNS | PCNSV | Primary central nervous system vasculitis | Primary vasculitis of the central nervous system

A rare medium or small vessel vasculitis characterized by focal and/or diffuse neurologic symptoms due to a documented arteritic process in the central nervous system in the absence of other identified underlying cause (infectious systemic other neurologic diseases etc.). It presents with non-specific symptoms of headache stroke or transient ischemic attacks with cognitive impairment hemiplegia weakness and rarely with cranial nerve involvement seizures and ataxia.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version February 2024

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