Primitive neuroectodermal tumor of the corpus uteri

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Synonyms: Malignant peripheral neuroectodermal tumor of the corpus uteri | Peripheral neuroectodermal cancer of the corpus uteri

Primitive neuroectodermal tumor of the corpus uteri is a rare cancer of corpus uteri derived from neural crest cells characterized by small round neoplastic cells with variable degree of neural glial and ependymal differentiation. Macroscopically the tumor is often a large poorly circumscribed polypoid mass with necrotic areas and hemorrhage. It usually presents with lower abdominal or pelvic pain irregular vaginal bleeding or discharge pelvic mass and uterine enlargement.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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