Proton-pump inhibitor-responsive esophageal eosinophilia

Get in touch with RARE Concierge.

Contact RARE Concierge

Proton-pump inhibitor-responsive esophageal eosinophilia

Synonyms: PPI-REE | PPI-responsive esophageal eosinophilia | PPIRee

Proton-pump inhibitor-responsive esophageal eosinophilia (PPI-REE) is a rare gastroenterologic disease characterized by typical clinical endoscopic and histological features of eosinophilic oesophagitis (i.e. symptomatic oesophageal dysfunction associated with eosinophil-predominant mucose infiltrate) which completely remits upon proton pump inhibitor therapy.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

Newly diagnosed with
Proton-pump inhibitor-responsive esophageal eosinophilia?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations


CURED is a not for profit foundation dedicated to those suffering from Eosinophilic Diseases. We are committed to raising substantial funding to aid in research, advocating on behalf of EGID patients & their families, & working to educate & increase awareness about this complex group of diseases. It is our heartfelt belief that CURED can make a difference for the individuals and their families.

Clinical Trials

For a list of clinical trials in this disease area, please click here.