Pseudoxanthoma elasticum-like papillary dermal elastolysis

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Synonyms: PXE-like papillary dermal elastolysis

Pseudoxanthoma elasticum-like papillary dermal elastolysis (PXE-PDE) is a rare acquired idiopathic dermal tissue disorder characterized by numerous asymptomatic 2-3 mm yellowish non-follicular papules that tend to converge into cobblestone-like plaques which are distributed symmetrically over the posterior neck supraclavicular region axillae and sometimes abdomen. Unlike PXE these skin lesions show select elimination (absence or marked loss) of elastic fibers in the papillary dermis and there is no systemic involvement.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version June 2024

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Clinical Trials

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