Punctate palmoplantar keratoderma type 2

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Synonyms: PPKP2 | PPPP | Porokeratosis punctata palmaris et plantaris | Punctate palmoplantar hyperkeratosis type 2

Punctate palmoplantar keratoderma type 2 is a type of isolated punctate hereditary palmoplantar keratoderma characterized by multiple asymptomatic 1 to 2 mm-long firm hyperkeratotic projections (‘spiny keratosis’) on the palms soles and digits (typically confined to their volar and/or lateral aspects). Histopathologically compact columnar parakeratosis over hypo- or agranular epidermis is observed.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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