A rare systemic disease characterized by persistent vomiting with confusion lethargy disorientation hyperreflexia hyperventilation and tachycardia with rapid progression to seizures non-inflammatory encephalopathy coma and death. It typically develops between 12 hours and 3 weeks after recovery from a viral illness such as upper respiratory tract infection or gastroenteritis. Hepatomegaly acute hepatic steatosis fatty liver degeneration and multiple laboratory abnormalities are associated.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024
Newly diagnosed with
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