Secondary intestinal lymphangiectasia
Secondary intestinal lymphangiectasia is an acquired from of intestinal lymphangiectasia (see this term) manifesting as a protein-losing enteropathy due to another disorder such as Crohns disease congestive heart failure sarcoidosis Turner syndrome (see these terms) and often in patients who have undergone a Fontan operation. It is characterized by malabsorption diarrhea edema due hypoproteinemia steatorrhea and serosal effusions.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Secondary intestinal lymphangiectasia?
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