TEMPI syndrome
Synonyms: Telangiectasia-erythrocytosis-monoclonal gammopathy-perinephric-fluid collections-intrapulmonary shunting syndrome
TEMPI syndrome is a rare multi-systemic disease characterized by the presence of Telangiectasias Erythrocytosis with elevated erythropoietin levels Monoclonal gammopathy Perinephric-fluid collections and Intrapulmonary shunting.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Clinical Trials
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