Torsade-de-pointes syndrome with short coupling interval
A rare variant of Torsade de pointes a polymorphic ventricular tachycardia which is characterized by a short coupling interval of the first TdP beat on electrocardiogram in the absence of any structural heart disease. It manifests in early adulthood with syncope often results in ventricular fibrillation and shows a high risk of sudden cardiac death.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Torsade-de-pointes syndrome with short coupling interval?
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