Tricuspid valve agenesis
Synonyms: Congenital unguarded tricuspid orifice
A rare congenital non-syndromic heart malformation characterized by partial or complete absence of tricuspid valve tissue and its apparatus with an existing orifice. It can be isolated or associated with other heart anomalies. Clinical presentation is variable and may include syncope arrhythmias cyanosis right heart dilatation and failure.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
Tricuspid valve agenesis?
Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.