Synonyms: Congenital unguarded tricuspid orifice
A rare congenital non-syndromic heart malformation characterized by partial or complete absence of tricuspid valve tissue and its apparatus with an existing orifice. It can be isolated or associated with other heart anomalies. Clinical presentation is variable and may include syncope arrhythmias cyanosis right heart dilatation and failure.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version September 2024
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Tricuspid valve agenesis?
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Clinical Trials
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