Synonyms: Follicular dyskeratoma
A rare benign epidermal disease characterized by a solitary asymptomatic verrucous skin-coloured to red-brown papule or nodule which contains a central pore and keratotic plug occuring most frequently on the scalp face and neck (rarely in the mouth under the nail plate or on the mons pubis). Occasionally lesions may be multiple and/or pruritic. Histologically a well-circumscribed cup-shaped keratin-filled invagination with prominent acantholytic dyskeratosis suprabasilar clefts and villi projecting into the clefts is observed.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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