Double-orifice mitral valve
A rare congenital non-syndromic heart malformation characterized by a single fibrous annulus with two orifices opening into the left ventricle. Clinical presentation is variable and related to the degree of resulting mitral insufficiency and/or stenosis and depending on the associated heart disease most commonly atrioventricular septal defect obstructive left-sided lesions and cyanotic heart disease. Rare cases of isolated disease have been reported.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
Double-orifice mitral valve?
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