Fibrohistiocytic inflammatory pseudotumor of the liver
A subtype of inflammatory pseudotumor of the liver characterized by a benign well-circumscribed tumor with fibrohistiocytic infiltration (including xanthogranulomatous inflammation multinucleated giant cells and neutrophilic infiltration) typically localized in the peripheral hepatic parenchyma. Presentation may be of non-specific symptoms (fever malaise and abdominal pain) or as an incidental finding.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
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Fibrohistiocytic inflammatory pseudotumor of the liver?
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Advocacy Organizations
Global Liver Institute
To improve the lives of individuals and families impacted by liver disease through promoting innovation, encouraging collaboration, and scaling optimal approaches to help eradicate liver diseases.
Clinical Trials
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