Lipomatous non-saccular limited dorsal myeloschisis

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Synonyms: Lipomatous flat LDM | Lipomatous flat limited dorsal myeloschisis | Lipomatous non-saccular LDM

A rare non-saccular limited dorsal myeloschisis histologically characterized by skin tissue with a jagged depression of squamous epithelium continued to subcutaneous mature adipose tissue with loose connective tissue. GFAP-immunopositive glial cells are embedded in the subcutaneous lipoma. The extradural and intradural stalk have cord-like fibrocollagenous tissue containing adipose tissue peripheral nerve fibers clusters of melanocytes and skeletal muscle fibers.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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Lipomatous non-saccular limited dorsal myeloschisis?

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