Lipomatous non-saccular limited dorsal myeloschisis
Synonyms: Lipomatous flat LDM | Lipomatous flat limited dorsal myeloschisis | Lipomatous non-saccular LDM
A rare non-saccular limited dorsal myeloschisis histologically characterized by skin tissue with a jagged depression of squamous epithelium continued to subcutaneous mature adipose tissue with loose connective tissue. GFAP-immunopositive glial cells are embedded in the subcutaneous lipoma. The extradural and intradural stalk have cord-like fibrocollagenous tissue containing adipose tissue peripheral nerve fibers clusters of melanocytes and skeletal muscle fibers.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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Lipomatous non-saccular limited dorsal myeloschisis?
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