Lymphoplasmacytic inflammatory pseudotumor of the liver

Get in touch with RARE Concierge.

Contact RARE Concierge

Lymphoplasmacytic inflammatory pseudotumor of the liver

Synonyms: IgG4-related inflammatory pseudotumor of the liver

A subtype of inflammatory pseudotumor of the liver characterized by a benign well-circumscribed tumor with diffuse lymphoplasmacytic infiltration with histological features of IgG4-related disease (numerous IgG4-positive plasma cells prominent eosinophils stromal fibrosis fibroblastic proliferations and frequently obliterative phlebitis) and that is likely located around the hepatic hilum. Most often it is discovered as an incidental finding.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. Ā© INSERM 1999. Available on http://www.orphadata.org. Data version December 2023

Newly diagnosed with
Lymphoplasmacytic inflammatory pseudotumor of the liver?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations

Clinical Trials

For a list of clinical trials in this disease area, please click here.