Lymphoplasmacytic inflammatory pseudotumor of the liver

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Synonyms: IgG4-related inflammatory pseudotumor of the liver

A subtype of inflammatory pseudotumor of the liver characterized by a benign well-circumscribed tumor with diffuse lymphoplasmacytic infiltration with histological features of IgG4-related disease (numerous IgG4-positive plasma cells prominent eosinophils stromal fibrosis fibroblastic proliferations and frequently obliterative phlebitis) and that is likely located around the hepatic hilum. Most often it is discovered as an incidental finding.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version June 2024

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Lymphoplasmacytic inflammatory pseudotumor of the liver?

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