Pleomorphic salivary gland adenoma

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Pleomorphic salivary gland adenoma

A rare tumor of salivary glands characterized by a benign well-circumscribed slow-growing painless mass most commonly occurring in the parotid gland (but also the palate submandibular gland or nasal septal mucosa) histopathologically composed of epithelial and myoepithelial / stromal components. Possible signs and symptoms depend on the location of the tumor and include facial nerve weakness mild dysphagia or unilateral nasal obstruction. Recurrence rates are low although tumor rupture and spillage have been reported. Malignant transformation may occur in a small percentage of cases.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version February 2024

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