Pulmonary artery hypoplasia

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Pulmonary artery hypoplasia

Synonyms: PAH | Unilateral Pulmonary Artery Hypoplasia

A rare congenital anomaly of the great arteries characterized by various clinical signs and symptoms including shortness of breath recurrent lower respiratory tract infections lung hypoplasia pulmonary hypertension and haemoptysis. The anomaly can be isolated or associated with congenital heart disease such as tetralogy of Fallot atrial septal defect coarctation of the aorta right aortic arch truncus arteriosus patent ductus arteriosus and pulmonary atresia.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.

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Pulmonary artery hypoplasia?

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Advocacy Organizations

Project FAVA

Project FAVA is a 501(c)(3) non-profit patient advocacy group that promotes awareness of fibro-adipose vascular anomalies, educates patients, their families, and the global community, and provides helpful resources to those with FAVA. Project FAVA also advances research to move the needle towards more effective and less invasive treatment options for FAVA patients.

Collaborative Research Advocacy for Vascular Anomalies Network (CaRAVAN)

As the research-based umbrella organization for all vascular anomalies, we are on a mission to develop a unified network of patients and their families, advocates, researchers, and clinicians who influence research from initial concept and design to patient care delivery

Clinical Trials

For a list of clinical trials in this disease area, please click here.