Pulmonary artery hypoplasia

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Synonyms: PAH | Unilateral Pulmonary Artery Hypoplasia

A rare congenital anomaly of the great arteries characterized by various clinical signs and symptoms including shortness of breath recurrent lower respiratory tract infections lung hypoplasia pulmonary hypertension and haemoptysis. The anomaly can be isolated or associated with congenital heart disease such as tetralogy of Fallot atrial septal defect coarctation of the aorta right aortic arch truncus arteriosus patent ductus arteriosus and pulmonary atresia.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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Pulmonary artery hypoplasia?

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Clinical Trials

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