Umbilical cord ulceration-intestinal atresia syndrome

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Umbilical cord ulceration-intestinal atresia syndrome

A rare syndromic intestinal malformation characterized by ulcer formation in the umbilical cord associated with congenital upper-intestinal atresia typically presenting with intra-uterine hemorrhaging from the ulcer site and subsequent fetal bradycardia.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024

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