A clinical variant of iridocorneal endothelial (ICE) syndrome characterized by progressive iris atrophy and holes present on the surface of the iris corneal edema corectopia uveal ectropion and anterior synechiae. Secondary glaucoma is also a common complication of the disease.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2026
Newly diagnosed with
Essential iris atrophy?
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