Synonyms: MCRCC | Multilocular clear cell adenocarcinoma | Multilocular clear cell carcinoma | Multilocular clear cell renal cell adenocarcinoma | Multilocular clear cell renal cell carcinoma | Multilocular cystic renal cell adenocarcinoma | Multilocular cystic renal cell carcinoma
Multilocular cystic renal neoplasm of low malignant potential is a rare subtype of clear cell renal cell carcinoma with distinct pathological features of cysts lined by occasionally flattened cuboidal clear cells and septa containing aggregates of epithelial cells with clear cytoplasm and excellent prognosis. The tumor usually presents as an asymptomatic unilateral solitary lesion macroscopically consisting of numerous fluid-filled septated cysts of variable size. Rarely the symptoms typically associated with renal tumors (flank pain hematuria palpable mass) may be present.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2026
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Multilocular cystic renal neoplasm of low malignant potential?
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