Congenital erosive and vesicular dermatosis
Synonyms: CEVD | Congenital erosive and vesicular dermatosis with reticulated supple scarring
A rare idiopathic skin disease characterized by widespread congenital superficial erosions and vesicles (often involving more than 75% of the body) which heal leaving scars with a supple symmetrical reticulated pattern frequently resulting in cicatricial alopecia and hyperthermia and/or hypohydrosis. Nail anomalies neurodevelopmental and ophtalmologic abnormalities tongue atrophy and preterm birth with or without history of choriomnionitis are commonly associated.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Congenital erosive and vesicular dermatosis?
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