Congenital panfollicular nevus is a rare benign skin tumor disorder characterized by the presence of congenital large (few centimeters) elevated well-circumscribed pink-tan multinodular non-ulcerative bosselated-surface skin lesions located on the neck scalp or hand and which enlarge with time. Histologically hamartomatous proliferation containing irregularly arranged malformed hair follicles in various stages of development surrounded by fibrous tissue and densely distributed within the dermis is observed.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2026
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Congenital panfollicular nevus?
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