Extraskeletal Ewing sarcoma

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Extraskeletal Ewing sarcoma

Synonyms: EOE | Extraosseous Ewing sarcoma | Extraosseous Ewing tumor | Extraskeletal Ewing tumor

Extraskeletal Ewing sarcoma is a rare poorly differentiated highly malignant soft tissue tumor derived from neuroectoderm that is morphologically indistinguishable from skeletal Ewing sarcoma but is located in extraosseous locations with the most common being: chest wall paravertebral region abdominopelvic area (with predilection for the retroperitoneal space) gluteal region and lower extremities. Clinical presentation is highly variable and depends on tumor localization. Local recurrence is common and metastatic disease most frequently involves the bones and lungs.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version May 2024

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Extraskeletal Ewing sarcoma?

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Advocacy Organizations

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


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Clinical Trials

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