Glomus tumor
A rare soft tissue tumor characterized by a nodular lesion composed of cells closely resembling the modified smooth muscle cells of the normal glomus body. The tumors most often arise in the skin or soft tissues of the distal extremities in particular the subungual region but have been reported in almost any location. They occur as typical glomus tumors glomangiomatosis (multiple nodules of solid glomus tumor investing the vascular walls) symplastic (showing striking nuclear atypia without mitotic activity or necrosis) or malignant glomus tumors and glomus tumors of uncertain malignant potential.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Glomus tumor?
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