A rare acquired dermis elastic tissue disease characterized by asymptomatic well-demarcated symmetric patches and/or plaques of finely wrinkled skin arranged parallel to skin cleavage lines (type I) associated with perifollicular papular protrusions (type II) or with persistent reticular erythema (type III) occurring predominantly on the shoulders trunk back and proximal extremities associating on histopathology a selective loss of elastic tissue in the midreticular dermis. Erythema and/or urticaria may or may not precede wrinkly lesions.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version November 2023
Newly diagnosed with
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