Synonyms: Pseudosarcomatous fasciitis | Pseudosarcomatous fibromatosis
A rare soft tissue tumor characterized by a solitary mass-forming fibrous proliferation that usually occurs in the subcutaneous tissue composed of uniform fibroblastic/myofibroblastic cells displaying a loose growth pattern. Upper extremities trunk and head and neck are most frequently affected. The lesion typically grows rapidly and almost always measures less than five centimeters in diameter. Macroscopically it may appear circumscribed or infiltrative but is not encapsulated. Recurrence after excision is very rare and metastasis does not occur.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2026
Newly diagnosed with
Nodular fasciitis?
Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.
Clinical Trials
For a list of clinical trials in this disease area, please click here.
