Synonyms: OODD
A rare genetic ectodermal dysplasia syndrome characterized by dental abnormalities (primarily agenesis of the permanent and deciduous teeth with cone-shaped incisors and canines) onychodysplasia palmoplantar hyperkeratosis dry skin and more variably hypotrichosis and sweat gland dysfunction (hyper- or hypohidrosis).
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2026
Newly diagnosed with
Odonto-onycho-dermal dysplasia?
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Advocacy Organizations
National Foundation for Ectodermal Dysplasias
Together, we enrich the lives of people affected by ectodermal dysplasias by fostering community, providing education and support, and driving advocacy and groundbreaking research—creating a brighter future for all.
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Clinical Trials
For a list of clinical trials in this disease area, please click here.