Primary Sjögren syndrome

Get in touch with RARE Concierge.

Contact RARE Concierge

Primary Sjögren syndrome

Synonyms: Primary Sjögren-Gougerot syndrome

A rare systemic autoimmune disease characterized by exocrine gland dysfunction resulting predominately in keratoconjunctivitis sicca and xerostomia but also affecting exocrine glands of the skin as well as respiratory urogenital and digestive tract. Extraglandular manifestations include arthritis interstitial lung disease renal disease and peripheral neuropathy. The disease is accompanied by a substantially increased risk to develop B-cell non-Hodgkin lymphoma especially MALT (mucosa-associated lymphoid tissue) lymphoma.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024

Newly diagnosed with
Primary Sjögren syndrome?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Clinical Trials

For a list of clinical trials in this disease area, please click here.