Progressive deafness with stapes fixation

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Synonyms: Progressive hearing loss with stapes fixation | Stapedo-vestibular ankylosis | Thies-Reis syndrome

Stapes fixation (stapedovestibular ankylosis) is a hearing loss condition that appears as a consequence of annular ligament destruction followed by excessive connective tissue production during the healing process. This condition is mainly observed in otosclerosis but is also found in chronic otitis media with tympanosclerosis and other rare bone diseases such as Paget’s disease and osteogenesis imperfecta (Lobstein disease).

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version June 2024

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Progressive deafness with stapes fixation?

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