Renal nutcracker syndrome

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Synonyms: Left renal vein entrapment syndrome | RNS

A rare syndromic renal disease characterized by the entrapment of left renal vein (LRV) between the superior mesenteric artery (SMA) and the abdominal aorta resulting in increased luminal pressure renal hilar varices hematuria and at the microscopic level rupture of thin-walled veins into the collecting system in renal fornices.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version May 2024

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Renal nutcracker syndrome?

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