Renal nutcracker syndrome

Get in touch with RARE Concierge.

Contact RARE Concierge

Renal nutcracker syndrome

Synonyms: Left renal vein entrapment syndrome | RNS

A rare syndromic renal disease characterized by the entrapment of left renal vein (LRV) between the superior mesenteric artery (SMA) and the abdominal aorta resulting in increased luminal pressure renal hilar varices hematuria and at the microscopic level rupture of thin-walled veins into the collecting system in renal fornices.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

Newly diagnosed with
Renal nutcracker syndrome?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations

Clinical Trials

For a list of clinical trials in this disease area, please click here.