Synonyms: Geographic helicoid peripapillary choroidopathy
A rare non-infectious posterior uveitis characterized by usually bilateral chronic progressive recurrent inflammation of the choroid retinal pigment epithelium and choriocapillaris. In the classic or peripapillary geographic type of the disease infiltrates originating in the peripapillary region progress in an irregular serpentine fashion centrifugally and resolve spontaneously after several weeks leaving atrophic scars. Multiple recurrences often with months to years of quiescence in between result in progressive visual loss in one or both eyes.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version October 2023.
Newly diagnosed with
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