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Somatostatinoma (SSoma) is an extremely rare pancreatic neuroendocrine tumor or duodenal endocrine tumor (see these terms) that originates either in the pancreas (50%) or the gastrointestinal tract (50%) and mainly presents with non-specific symptoms of abdominal pain weight loss jaundice and diarrhea but in approximately 20% of pancreatic cases leads to a somatostatin hypersecretion syndrome (somatostatinoma syndrome) characterized by diabetes mellitus cholelithiasis steatorrhea and hypochlorhydria.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version July 2024

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Clinical Trials

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