Striate palmoplantar keratoderma
Synonyms: Keratosis palmoplantaris striata | Keratosis palmoplantaris striata et areata | Keratosis palmoplantaris varians of Wachters
Striate palmoplantar keratoderma is an isolated focal hereditary palmoplantar keratoderma characterized by linear hyperkeratosis along the flexor aspect of the fingers and on palms as well as focal hyperkeratosis of the plantar skin. Patients present with painful thickening of the skin on palms and soles with occasional fissuring blistering and hyperhidrosis. Rarely hyperkeratosis on other areas may be seen (knees dorsal aspects of the digits). Histopatologically widened intercellular spaces between keratinocytes are observed.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version December 2023
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Striate palmoplantar keratoderma?
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