Terrien marginal degeneration
A rare disorder of the anterior segment of the eye characterized by slowly progressive bilateral asymmetric usually non-inflammatory degeneration of the peripheral cornea resulting in stromal thinning vascularization lipid deposition and against-the-rule astigmatism with decreased visual acuity. Degeneration typically involves the superior aspect of the cornea first and extends circumferentially leading to circumferential ectasia of the peripheral cornea. Opacification of the central cornea may occur at a very advanced stage. In rare cases the condition is complicated by perforation.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
Newly diagnosed with
Terrien marginal degeneration?
Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.