Autoimmune hepatitis type 1

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Autoimmune hepatitis type 1

Synonyms: AIH type 1

A form of autoimmune hepatitis characterized by clinical presentation as cryptogenic hepatitis interface hepatitis on histological examination elevated serum aminotransferase levels hypergammaglobulinemia/elevated immunoglobulin G and presence of circulating autoantibodies specifically antinuclear antibodies (ANA) anti-smooth muscle antibodies (anti-SMA) and/or anti-soluble liver antigen/liver pancreas antigen antibodies (anti-SLA/LP). The disease predominantly develops at a post-pubertal age and most commonly takes a chronic course although acute or acute severe presentation may also be observed. Typical concurrent autoimmune diseases are autoimmune thyroiditis and rheumatic diseases.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on Data version April 2024

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