Autoimmune hepatitis type 2

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Autoimmune hepatitis type 2

Synonyms: AIH type 2

A form of autoimmune hepatitis characterized by clinical presentation as cryptogenic hepatitis interface hepatitis on histological examination elevated serum aminotransferase levels hypergammaglobulinemia/elevated immunoglobulin G and presence of circulating autoantibodies specifically antibodies to liver kidney microsome type 1 (anti-LKM1) and anti-liver cytosol type 1 (anti-LC1) antibodies. The disease typically manifests in childhood or adolescence with an acute onset often with acute liver failure. Long-term immunosuppression is usually required. Reported concurrent autoimmune diseases are autoimmune thyroiditis diabetes mellitus and vitiligo.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

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