Autoimmune pancreatitis type 1
Synonyms: AIP type 1 | IgG4-related pancreatitis | Lymphoplasmacytic sclerosing pancreatitis
Type 1 autoimmune pancreatitis is a form of autoimmune pancreatitis seen in elderly males (>60 years) and presenting with abdominal pain steatorrhea obstructive jaundice and other organ (bile duct kidneys and retroperitoneum) involvement. It is thought to be due to an immunoglobulin G4 (IgG4)-associated systemic disease.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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Autoimmune pancreatitis type 1?
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