Autoimmune pancreatitis type 1

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Autoimmune pancreatitis type 1

Synonyms: AIP type 1 | IgG4-related pancreatitis | Lymphoplasmacytic sclerosing pancreatitis

Type 1 autoimmune pancreatitis is a form of autoimmune pancreatitis seen in elderly males (>60 years) and presenting with abdominal pain steatorrhea obstructive jaundice and other organ (bile duct kidneys and retroperitoneum) involvement. It is thought to be due to an immunoglobulin G4 (IgG4)-associated systemic disease.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

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Autoimmune pancreatitis type 1?

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