IgG4-related ophthalmic disease

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A rare inflammatory eye disease characterized by IgG4-immunopositive lymphocyte and plasmacyte infiltration and collagenous fibrosis of affected tissue and elevated serum levels of IgG4. Clinical presentation includes mass lesion or swelling of the involved structures commonly involving lacrimal gland and duct infraorbital and supraorbital nerves extraocular muscles and orbital soft tissues. A systemic involvement is common.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview. Reference: Access aggregated data from Orphanet at Orphadata. Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version May 2024

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IgG4-related ophthalmic disease?

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