Dentinogenesis imperfecta
Synonyms: DGI | DGI without OI | DI | Dentinogenesis imperfecta without osteogenesis imperfecta | Non-syndromic DGI | Non-syndromic dentinogenesis imperfecta | Opalescent teeth without OI | Opalescent teeth without osteogenesis imperfecta
Dentinogenesis imperfecta (DGI) is a hereditary dentin defect (see this term) characterized by abnormal dentin structure resulting in abnormal tooth development.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
Newly diagnosed with
Dentinogenesis imperfecta?
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