Dentinogenesis imperfecta type 3
Synonyms: Dentinogenesis imperfecta, Shields type 3
Dentinogenesis imperfecta type 3 (DGI-3) is a rare severe form of dentinogenesis imperfecta (DGI see this term) characterized by opalescent primary and permanent teeth marked attrition large pulp chambers multiple pulp exposure and shell teeth radiographically (i.e. teeth which appear hollow due to dentin hypotrophy).
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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Dentinogenesis imperfecta type 3?
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