Type of disease: Rare conditions
Dermatofibrosarcoma protuberans is an uncommon tumor that arises in the skin. The tumor is firm and often flesh-colored although it can be reddish, bluish, or purplish. The tumor is often found on the chest or shoulders, but it can be found on other parts of the body. Dermatofibrosarcoma protuberans may cause no symptoms, and the initial size of the tumor tends to be around 1 to 5 centimeters. This tumor has a low potential to spread to other tissues. Treatment often involves surgery to remove the tumor, such as by Mohs’ micrographic surgery. If you or a family member has been diagnosed with dermatofibrosarcoma protuberans, talk with your doctor about the most current treatment options.Source: Genetic and Rare Diseases Information Center (GARD), supported by ORDR-NCATS and NHGRI.