Acinar cell carcinoma of pancreas

Get in touch with RARE Concierge.

Contact RARE Concierge

Acinar cell carcinoma of pancreas

Synonyms: Pancreatic acinar cell carcinoma

A very rare malignant epithelial tumor of the pancreas characterized macroscopically by a usually large well-circumscribed fully or partially encapsulated solid mass often with hemorrhage necrosis and cystic changes in any portion of the pancreas and histologically by neoplastic cells with variable degrees of differentiation and morphology ranging from acinar structures similar to normal pancreatic acini to large sheets of poorly differentiated neoplastic cells. Presenting symptoms are typically non-specific and include abdominal pain weight loss vomiting nausea and/or less commonly jaundice. Immunohistochemical evidence of acinar-specific products is observed. Association with Lynch syndrome familial adenomatous polyposis and pancreatic panniculitis has been reported.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version October 2023.

Newly diagnosed with
Acinar cell carcinoma of pancreas?

Our RARE Concierge Services Guides are available to assist you by providing information, resources and connections as you navigate your rare disease journey.

Get Concierge Help

Advocacy Organizations

My Faulty Gene

My Faulty Gene is a nonprofit organization which provides information and assistance to any individual whose family medical history suggests genetic testing might be helpful in identifying an increased risk of disease due to a genetic mutation. We believe that everyone in need of genetic testing should have access to it.

My Little Sunshine Foundation

My Little Sunshine is a non-profit foundation dedicated to educating people about the importance of fertility preservation and making fertility resources accessible to all.


Educate and provide resources to POC with Rare Cancers

Clinical Trials

For a list of clinical trials in this disease area, please click here.