Bilateral striopallidodentate calcinosis
Synonyms: BSPDC | Cerebrovascular ferrocalcinosis | Idiopathic basal ganglia calcification | PFBC | Primary familial brain calcification
Bilateral striopallidodentate calcinosis (BSPDC also erroneously called Fahr disease) is characterized by the accumulation of calcium deposits in different brain regions particularly the basal ganglia and dentate nucleus and is often associated with neurodegeneration.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: //www.orphadata.org. Data version September 2023.
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Bilateral striopallidodentate calcinosis?
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