Bilateral striopallidodentate calcinosis

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Bilateral striopallidodentate calcinosis

Synonyms: BSPDC | Cerebrovascular ferrocalcinosis | Idiopathic basal ganglia calcification | PFBC | Primary familial brain calcification

Bilateral striopallidodentate calcinosis (BSPDC also erroneously called Fahr disease) is characterized by the accumulation of calcium deposits in different brain regions particularly the basal ganglia and dentate nucleus and is often associated with neurodegeneration.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http: // Data version September 2023.

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Bilateral striopallidodentate calcinosis?

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Advocacy Organizations

The Assistance Fund

The Assistance Fund (TAF) is an independent charitable patient assistance organization that helps patients and families facing high medical out-of-pocket costs by providing financial assistance for their copayments, coinsurance, deductibles, and other health-related expenses. We currently manage more than 80 disease programs, each of which covers all FDA-approved treatment for the disease named in the program. Since 2009, TAF has helped nearly 180,000 people access critical treatment for life-threatening, chronic, and rare diseases.

Clinical Trials

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