Chronic relapsing inflammatory optic neuropathy

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Chronic relapsing inflammatory optic neuropathy

Synonyms: CRION | Chronic recurrent isolated optic neuritis

A rare inflammatory optic neuropathy characterized by severe and persistent pain followed by subacute visual loss a relapsing-remitting course and steroid-dependence. Involvement of both optic nerves is common and is usually sequential. Serum antibodies against aquaporin 4 are absent in most cases. Magnetic resonance imaging shows contrast enhancement of the acutely inflamed optic nerves.

Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.

Reference: Access aggregated data from Orphanet at Orphadata.

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024

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Clinical Trials

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