Congenital anomaly of the tricuspid valve chordae
Synonyms: Congenital anomaly of tricuspid chordae tendineae | Congenital anomaly of tricuspid tendinous chords
A rare congenital anomaly of the tricuspid subvalvular apparatus characterized by aberrant tendinous chords which insert at the clear zone of the leaflet instead of its free edge and connect to the endocardium instead of the papillary muscles. Resulting tethering of one or more tricuspid leaflets leads to their impaired mobility and tricuspid regurgitation. Association with other congenital cardiac anomalies has been reported.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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